E-ISSN: 1308-5263
A rare syndrome that can easily be missed: May-Hegglin anomaly [Turk J Hematol]
Turk J Hematol. 2005; 22(2): 91-93

A rare syndrome that can easily be missed: May-Hegglin anomaly

İsmet Aydoğdu, Emin Kaya, İrfan Kuku, M. Ali Erkurt, Ahmet Görgel, Onur Özhan
Department Of Hematology, İnönü University School Of Medicine, Malatya, Turkey

May-Hegglin is a rare disease characterized by macrothrombocytopenia and presence of Döhle-like bodies in white cells. We present a patient treated with acute myeloid leukemia had pale-blue colored inclusion bodies assuming Döhle in his neutrophils.

Keywords: May-Hegglin, Thrombocytopenia, Leukemia.

Tanı zorluğu olabilecek seyrek bir sendrom: May-Hegglin anomalisi

İsmet Aydoğdu, Emin Kaya, İrfan Kuku, M. Ali Erkurt, Ahmet Görgel, Onur Özhan
Department Of Hematology, İnönü University School Of Medicine, Malatya, Turkey

May-Hegglin makrotrombositopeni ve lökositlerde Döhle benzeri cisimciklerle karakterize seyrek görülen bir hastalıktır. Akut miyeloblastik lösemi nedeniyle tedavi ettiğimiz, lökositlerinde soluk-mavi renkli, Döhle cisimcikleri olduğunu düşündüğümüz bir hasta takdim ediyoruz.

Anahtar Kelimeler: May-Hegglin, Trombositopeni, Lösemi.

Corresponding Author: İsmet Aydoğdu, Türkiye
Manuscript Language: English
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